Cistic Fibrosis by Jamie Manus https://padlet.com/jlmanus0317/got3rf0q85ss NURV 307 Journal Assignment en-us 2018-01-19 17:02:09 UTC 2026-03-23 19:26:08 UTC hello@padlet.com Clinical Manifestations jlmanus0317 https://padlet.com/jlmanus0317/got3rf0q85ss/wish/224471401 In younger people you can expect to see:
  • clubbing of the fingers and toes
  • cyanosis
  • chronic purulent discharge from the nose
  • recurrent episodes of bronchitis and bronchopneumonia
  • chronic weight and nutritional problems
]]> 2018-01-24 23:00:06 UTC https://padlet.com/jlmanus0317/got3rf0q85ss/wish/224471401 The Breakdown: jlmanus0317 https://padlet.com/jlmanus0317/got3rf0q85ss/wish/224472310 Cystic Fibrosis is a genetic disease. This leads to the body producing to much mucus that is really thick and unwavering. It not only effects the respiratory system but also the GI and reproductive as well.]]> 2018-01-24 23:06:54 UTC https://padlet.com/jlmanus0317/got3rf0q85ss/wish/224472310 Diagnostic Criteria jlmanus0317 https://padlet.com/jlmanus0317/got3rf0q85ss/wish/224475351
  • Blood testing that looks for an elevated serum level of the pancreatic enzyme trypsinogen, especially in newborns.
  • Sweat chloride test which simulates the production of sweat, then measures the amount of sweat electrolytes. Normal is less than 40 mEq/L and greater than 60 mEq/L would indicate Cystic Fibrosis.
    • ]]>     2018-01-24 23:30:01 UTC https://padlet.com/jlmanus0317/got3rf0q85ss/wish/224475351     Do you have the gene? jlmanus0317 https://padlet.com/jlmanus0317/got3rf0q85ss/wish/224476855 Men and women are equally affected however, more white people get Cystic Fibrosis then other races. 40% of these patients in the United States are 18 or older. 80% of Cystic Fibrosis patients are diagnosed under age 3, as early as 2 days old.]]> 2018-01-24 23:43:54 UTC https://padlet.com/jlmanus0317/got3rf0q85ss/wish/224476855 Treatments and Medications jlmanus0317 https://padlet.com/jlmanus0317/got3rf0q85ss/wish/224477934 The goal of treatments are to help patients with Cystic Fibrosis cough up all the mucus. There are four ways to to this.
    1. Chest Physiotherapy - done twice a day, morning and evening.
    2. Postural Drainage and Percussion - each lobe of the lungs needs to be percussed for 3-5 minutes. This can be done by a parent or a nurse if they are hospitalized.
    3. Positive Expiratory Pressure - uses a breathing devise with a special expiratory valve that creates a positive pressure in the airways while exhaling.
    4. Flutter Mucus Clearance Device - a small handheld plastic pipe with a mouthpiece and a stainless-steel ball inside.
    5. Surgery may be necessary to remove a bowel obstruction.
    A lung transplant could be an option but it is not very successful. 90% survive one year, and 50% survive at least five years.
    For the GI system:
    • Lactulose (prevents constipation)
    • Ursodeoxycholic Acid - used to treat and possibly prevent progressive liver disease.
    For the Respiratory System:
    • Bronchodilators used before chest physiotherapy.
    • Dornase Alfa (Pulmozyme) - improve pulmonary function and decrease risk of infection.
    • Aerosol antibiotics (gentamicin, ticarcillin, tobramycin) - given via nebulizer after chest physiotherapy
    ]]>     2018-01-24 23:54:02 UTC https://padlet.com/jlmanus0317/got3rf0q85ss/wish/224477934     Flutter Mucus Clearance Device jlmanus0317 https://padlet.com/jlmanus0317/got3rf0q85ss/wish/224479562 2018-01-25 00:11:18 UTC https://padlet.com/jlmanus0317/got3rf0q85ss/wish/224479562 Complications jlmanus0317 https://padlet.com/jlmanus0317/got3rf0q85ss/wish/224481534 Respiratory problems
    • Hemothorax, pneumothorax or even atelectasis can occur.
    Gastroesophageal reflux disease
    Pancreatic problems 
    • Blocked pancreatic ducts can lead to pancreatitis.
    Intestinal obstruction
    Diabetes
    Reproductive problems
    • Most men are sterile due to the mucus blocking sperm in the vas deferens.
    • Women may experience difficulty getting pregnant the traditional way. Optional ways are artificial insemination and in vitro fertilization.
    ]]>     2018-01-25 00:28:03 UTC https://padlet.com/jlmanus0317/got3rf0q85ss/wish/224481534     Nursing Interventions jlmanus0317 https://padlet.com/jlmanus0317/got3rf0q85ss/wish/224483845
  • Encourage your female patients that are considering pregnancy to get tested to see if they are a carrier of the mutated gene.
  • Let parents know that children tend to bruise easily due to their inability to absorb fat-soluble vitamins.
  • Encourage Cystic Fibrosis patients to include daily exercise in their routine to stimulate coughing.
  • Teach your patients and their parents about support groups
  • Watch for signs and symptoms of the other complications that can arise with Cystic Fibrosis.
    • ]]>     2018-01-25 00:47:05 UTC https://padlet.com/jlmanus0317/got3rf0q85ss/wish/224483845     Quiz Time jlmanus0317 https://padlet.com/jlmanus0317/got3rf0q85ss/wish/224487364 1. The nurse performs a sweat chloride test on a patient and the result was 72 mEq/L. This is an indicator that the patient has:
    a. Diaphoresis
    b. COPD
    c. Cystic Fibrosis
    d. GERD

    2. When doing chest physiotherapy including postural drainage and percussion, how long should each section of the lungs be percussed?
    a. 1-3 minutes
    b. 3-5 minutes
    c. 8-10 minutes
    d. 10-15 minutes

    3. Can Cystic Fibrosis be cured?
    a. Yes
    b. No

    4. Patients with Cystic Fibrosis should increase what in their diet?
    a. Sugar
    b. Protein
    c. Fat
    d. Salt

    5. Cystic Fibrosis affects the following systems: (select all that apply)
    a. Respiratory
    b. Cardiac
    c. Reproductive
    e. Gastrointestinal
    f. Endocrine]]>     2018-01-25 01:16:13 UTC https://padlet.com/jlmanus0317/got3rf0q85ss/wish/224487364     Reference jlmanus0317 https://padlet.com/jlmanus0317/got3rf0q85ss/wish/224490071 Gardner, J. (2007). What you need to know about cystic fibrosis. Nursing 2007, p. 52-55.

     

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